嗜鉻細(xì)胞瘤是來源于神經(jīng)嵴的產(chǎn)生兒茶酚胺的腫瘤。原發(fā)性心臟嗜鉻細(xì)胞瘤是極為罕見的，全世界目前見于文獻(xiàn)報(bào)道的僅為100例左右，北京協(xié)和醫(yī)院心外科去年1月份成功進(jìn)行了一例心臟嗜鉻細(xì)胞瘤切除手術(shù)，患者為中年女性，腫瘤同時侵犯左右心房，其MIBG閃爍掃描的結(jié)果正常，但奧曲肽顯像結(jié)果異常。腫瘤在體外循環(huán)下被成功切除。該病例報(bào)告已經(jīng)發(fā)表在著名心胸外科專業(yè)雜志Annals of Thoracic Surgery上。

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　　Fig 1. (A) 99m-Technetium-labeled hydrazinonicotinyl-Tyr3-octretide scintiscan demonstrated a focus of intense uptake on right side of heart silhouette. (B) Contrast-enhanced computed tomographic scan illustrated tumor (arrow) overlying interatrial groove. (LA = left atrium; RA = right atrium.)

　　Fig 2. Coronary angiogram demonstrated a tumor blush with 2 feeding vessels (white arrows) branching from left circumflex artery.

　　Fig 3. Resected cardiac pheochromocytoma.

　　Primary Cardiac Pheochromocytoma Involving Both Right and Left Atria

　　Xingrong Liu, MD, Qi Miao, MD , Heng Zhang, MD, Chaoji Zhang, MD, Lihua Cao, MD, Guotao Ma, MD, Zhengpei Zeng, MD

　　Pheochromocytomas are catecholamine-producing paragangliomas derived from the neural crest. Primary cardiac pheochromocytoma is extremely rare. We describe a case of cardiac pheochromocytoma involving both right and left atria in a middle-aged woman. Metaiodobenzylguanidine (MIBG) scintiscan results were normal, but results from an octreotide scan were abnormal. The tumor was successfully resected using cardiopulmonary bypass (CPB).

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